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dc.contributor.authorFleck, Tatiana-
dc.contributor.authorWolner, E.-
dc.contributor.authorGrabenwoger, M.-
dc.contributor.authorCzerny, M.-
dc.date.accessioned2015-07-10T09:55:17Z-
dc.date.available2015-07-10T09:55:17Z-
dc.date.issued2004-
dc.identifier.citationImages in Paediatric Cardiology. 2004, Vol.6(2), p. 1-11en_GB
dc.identifier.urihttps://www.um.edu.mt/library/oar//handle/123456789/3989-
dc.description.abstractMarfan syndrome is an autosomal dominant heritable connective tissue disorder which involves primarily the skeletal, ocular and cardiovascular system. The incidence of MS is on average 1: 10000 with 25-30% of cases caused by sporadic mutations. The leading cause of premature death in these patients is progressive dilatation and subsequent dissection of the ascending thoracic aorta resulting in cardiac tamponade, and left ventricular failure due to aortic regurgitation. Life expectancy is primarily determined by the severity of cardiovascular involvement, and has improved substantially over the last 20 years due to the advances in surgical and medical management. The optimum management of Marfan patients includes a lifelong surveillance with particular emphasis placed on aortic behaviour. Preventive replacement of various portions of the aorta has been a major contribution for improved life expectancy in these patients. The different surgical and interventional treatment options currently available will be further outlined in this review.en_GB
dc.language.isoenen_GB
dc.publisherImages in Paediatric Cardiologyen_GB
dc.rightsinfo:eu-repo/semantics/openAccessen_GB
dc.subjectMarfan syndromeen_GB
dc.subjectThoracic surgical proceduresen_GB
dc.subjectLife expectancyen_GB
dc.titleInterventional treatment methods in patients with Marfan Syndromeen_GB
dc.typearticleen_GB
dc.rights.holderThe copyright of this work belongs to the author(s)/publisher. The rights of this work are as defined by the appropriate Copyright Legislation or as modified by any successive legislation. Users may access this work and can make use of the information contained in accordance with the Copyright Legislation provided that the author must be properly acknowledged. Further distribution or reproduction in any format is prohibited without the prior permission of the copyright holder.en_GB
dc.description.reviewedpeer-revieweden_GB
Appears in Collections:IPC, Volume 6, Issue 2
IPC, Volume 6, Issue 2

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